Dyke Davidoff Masson Syndrome with Abdominal Epilepsy-Rare Presentation

Authors

  • Shitanshu Srivastava Department of Pediatrics, Era’s Lucknow Medical College, Lucknow
  • Rajat Pratap Singh Department of Pediatrics, Era’s Lucknow Medical College, Lucknow
  • KL Srivastava Department of Pediatrics, Era’s Lucknow Medical College, Lucknow

DOI:

https://doi.org/10.3126/ajms.v3i2.6172

Keywords:

Dyke Davidoff Masson syndrome, abdominal epilepsy, cerebral hemiatrophy, mental retardation

Abstract

Dyke Davidoff Masson Syndrome (DDMS) with abdominal epilepsy, is a rare clinical condition. It is characterized by severe abdominal pain with seizures, facial asymmetry, contralateral hemiparesis, and mental retardation. Diagnosis is made clinically coupled with radiological features which include cerebral hemiatrophy with homolateral hypertrophy of the skull and sinuses along with abnormal EEG and response to antiepileptic drugs. Here we report a case of DDMS with abdominal epilepsy in a 10 year old male child who presented with recurrent episodes of severe abdominal pain followed by seizures, hemiparesis and mental retardation. CT and MRI showed hemiatrophy of right cerebral hemisphere.

DOI: http://dx.doi.org/10.3126/ajms.v3i2.6172

Asian Journal of Medical Sciences 3(2012) 25-28

Downloads

Download data is not yet available.
Abstract
623
PDF
963

Downloads

Additional Files

Published

2013-02-26

How to Cite

Srivastava, S., Singh, R. P., & Srivastava, K. (2013). Dyke Davidoff Masson Syndrome with Abdominal Epilepsy-Rare Presentation. Asian Journal of Medical Sciences, 3(2), 25–28. https://doi.org/10.3126/ajms.v3i2.6172

Issue

Vol. 3 No. 2 (2012)

Section

Case Reports

License

Authors who publish with this journal agree to the following terms:

  1. The journal holds copyright and publishes the work under a Creative Commons CC-BY-NC license that permits use, distribution and reprduction in any medium, provided the original work is properly cited and is not used for commercial purposes. The journal should be recognised as the original publisher of this work.
  2. Authors are able to enter into separate, additional contractual arrangements for the non-exclusive distribution of the journal's published version of the work (e.g., post it to an institutional repository or publish it in a book), with an acknowledgement of its initial publication in this journal.
  3. Authors are permitted and encouraged to post their work online (e.g., in institutional repositories or on their website) prior to and during the submission process, as it can lead to productive exchanges, as well as earlier and greater citation of published work (See The Effect of Open Access).