Kartagener Syndrome: Congenital Variety of Primary Ciliary Dyskinesia with Infertility

Authors

  • Amit Nandan Dhar Dwivedi Subharati Medical College, Swami Vivekanand Subharati University, Meerut, India

DOI:

https://doi.org/10.3126/ajms.v1i1.2605

Keywords:

Immotile cilia syndrome, primary ciliary dyskinesia (PCD), situs inversus, chronic sinusitis, bronchiectasis

Abstract

We report a rare case of Kartagener's Syndrome, congenital variety of Primary Ciliary Dyskinesia (PCD) with infertility. The patient exhibited the classical triad of which was elucidated by Manes Kartagener in 1933. The frequency of KS in the United States is 1 case per 32,000 live births. Situs inversus occurs randomly in half the patients with PCD; therefore, for every patient with KS, another patient has PCD but not situs inversus.  Current nomenclature classifies all congenital ciliary disorders as PCDs in order to differentiate them from acquired types. KS is part of the larger group of disorders referred to as PCDs. Approximately one half of patients with PCD have situs inversus and, thus, are classified as having KS.

Keywords: Immotile cilia syndrome; Primary ciliary dyskinesia (PCD); Situs inversus; Chronic sinusitis; Bronchiectasis.

DOI: 10.3126/ajms.v1i1.2605

Asian Journal of Medical Sciences Vol.1(1) 2010 p.16-17

Downloads

Download data is not yet available.
Abstract
937
PDF
613

Author Biography

Amit Nandan Dhar Dwivedi, Subharati Medical College, Swami Vivekanand Subharati University, Meerut, India


Assistant Professor,
Department of Radiology
Subharati Medical College,
Swami Vivekanand Subharati University, Meerut, India

Downloads

Published

2010-05-07

How to Cite

Dwivedi, A. N. D. (2010). Kartagener Syndrome: Congenital Variety of Primary Ciliary Dyskinesia with Infertility. Asian Journal of Medical Sciences, 1(1), 16–17. https://doi.org/10.3126/ajms.v1i1.2605

Issue

Vol. 1 No. 1 (2010)

Section

Original Articles

License

Authors who publish with this journal agree to the following terms:

  1. The journal holds copyright and publishes the work under a Creative Commons CC-BY-NC license that permits use, distribution and reprduction in any medium, provided the original work is properly cited and is not used for commercial purposes. The journal should be recognised as the original publisher of this work.
  2. Authors are able to enter into separate, additional contractual arrangements for the non-exclusive distribution of the journal's published version of the work (e.g., post it to an institutional repository or publish it in a book), with an acknowledgement of its initial publication in this journal.
  3. Authors are permitted and encouraged to post their work online (e.g., in institutional repositories or on their website) prior to and during the submission process, as it can lead to productive exchanges, as well as earlier and greater citation of published work (See The Effect of Open Access).