Sturge Weber Syndrome With Posterior Fossa Involvement : A Rare Case

Abstract

Sturge-Weber syndrome (SWS) is a rare congenital vascular disorder characterized by facial capillary malformation, associated capillary-venous malformations affecting the brain and eye along with calcification in the occipital or frontoparietal region. Occipital and posterior parietal lobes are the common site of involvement in SWS. Posterior fossa involvement is a rare finding with very few number of reported cases. Contrast enhanced MRI is considered as the gold standard for the diagnosis of SWS demonstrating the enhancement of pial angioma