Recurrent Pneumonias and Bronchiectasis - Is it an Immunodeficiency Disorder? - A Case Report

Authors

  • Sumit Agrawal Department of Paediatrics, Kanti Children’s Hospital, Maharajgunj, Kathmandu, Nepal 
  • S Shreeram Department of Paediatrics, Kanti Children’s Hospital, Maharajgunj, Kathmandu, Nepal 
  • A Jha Department of Paediatrics, Kanti Children’s Hospital, Maharajgunj, Kathmandu, Nepal 
  • B Prajapati Department of Paediatrics, Kanti Children’s Hospital, Maharajgunj, Kathmandu, Nepal 

DOI:

https://doi.org/10.3126/jnps.v40i2.29625

Keywords:

Common variable immunodeficiency, cytopenias, fungal pneumonia, recurrent pneumonia

Abstract

Common Variable Immunodeficiency (CVID) is a form of primary immunodeficiency disorder characterised by hypogammaglobulinemia and recurrent sino-pulmonary infections. Its diagnosis is based on the presence of low serum IgG (< 2 SD below normal for age) with or without low IgA/ IgM levels and presentation beyond two years of age. These children also have disorders of autoimmunity with majority of them presenting as autoimmune cytopenias, predominantly thrombocytopenia and some having anaemia and neutropenias. Here we report a nine years old boy with past history of recurrent pneumonia, presenting this episode with fungal pneumonia, thrombocytopenia and anaemia eventually diagnosed as CVID.

Downloads

Download data is not yet available.
Abstract
172
PDF
221
Cover JNPS

Downloads

Published

2020-09-11

How to Cite

Agrawal, S., Shreeram, S., Jha, A., & Prajapati, B. (2020). Recurrent Pneumonias and Bronchiectasis - Is it an Immunodeficiency Disorder? - A Case Report. Journal of Nepal Paediatric Society, 40(2), 139–142. https://doi.org/10.3126/jnps.v40i2.29625

Issue

Vol. 40 No. 2 (2020)

Section

Case Reports

License

Authors who publish with this journal agree to the following terms:

Authors retain copyright and grant the journal right of first publication with the work simultaneously licensed under a Creative Commons Attribution License that allows others to share the work with an acknowledgement of the work's authorship and initial publication in this journal.

Authors are able to enter into separate, additional contractual arrangements for the non-exclusive distribution of the journal's published version of the work (e.g., post it to an institutional repository or publish it in a book), with an acknowledgement of its initial publication in this journal.

Authors are permitted and encouraged to post their work online (e.g., in institutional repositories or on their website) prior to and during the submission process, as it can lead to productive exchanges, as well as earlier and greater citation of published work (See The Effect of Open Access).