Congenital chylothorax in a preterm infant with non-immune hydrops: A case report with literature review on treatment options

Authors

DOI:

https://doi.org/10.3126/jkmc.v12i2.60349

Keywords:

Congenital chylothorax, hydrops fetalis, Octreotide, Sildenafil

Abstract

Congenital chylothorax is rare with an incidence of 1:10,000-24,000 live births. Congenital chylothorax occurs in lymphatic disorders, heart diseases, cancers, chromosomal abnormalities, tracheoesophageal fistula, etc. Acquired causes are due to surgical thoracic duct trauma. Many cases of chylothorax are idiopathic. The case fatality rate is 15% to 57% and reaches 98% in hydrops foetalis. There is no set standard of treatment for congenital chylothorax. Prenatally, thoracentesis or pleuro-amniotic shunts are done. Postnatally, management of cause, drainage, dietary changes, Octreotide, and Sildenafil have variable results. Pleurodesis, pleuroperitoneal shunt, abrasion, thoracic duct ligation, and anastomoses are surgical options.

Downloads

Download data is not yet available.
Abstract
121
PDF
132

Downloads

Published

2023-06-30

How to Cite

Raya, G. B., Basnet, S. ., & Nyaupane, S. (2023). Congenital chylothorax in a preterm infant with non-immune hydrops: A case report with literature review on treatment options. Journal of Kathmandu Medical College, 12(2), 116–123. https://doi.org/10.3126/jkmc.v12i2.60349

Issue

Vol. 12 No. 2 (2023): Issue 44, Apr-Jun 2023

Section

Case Reports

License

Creative Commons License

This work is licensed under a Creative Commons Attribution-NonCommercial 4.0 International License.

Copyright © Journal of Kathmandu Medical College
The ideas and opinions expressed by authors or articles summarized, quoted, or published in full text in this journal represent only the opinions of the authors and do not necessarily reflect the official policy of Journal of Kathmandu Medical College or the institute with which the author(s) is/are affiliated, unless so specified.

Authors convey all copyright ownership, including any and all rights incidental thereto, exclusively to JKMC, in the event that such work is published by JKMC. JKMC shall own the work, including 1) copyright; 2) the right to grant permission to republish the article in whole or in part, with or without fee; 3) the right to produce preprints or reprints and translate into languages other than English for sale or free distribution; and 4) the right to republish the work in a collection of articles in any other mechanical or electronic format.